A
methionine-free powdered medical food for the dietary management
of vitamin B6 non-responsive homocystinuria or hypermethioninemia in individuals over the age of one year.
This formulation is available in the US and Canada.
Main Features:
Methionine-free
Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, select vitamins, minerals and trace elements
Methionaid provides 60 g of protein equivalent per 100 g of powder
Unflavored powder
Does not contain fat thereby allowing greater flexibility in modifying energy intake
Indications:
Vitamin B6 non-responsive homocystinuria
Hypermethioninemia
Directions for Preparation and Use:
Methionaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a dietitian or physician to meet protein and general nutrition requirements. Fat, carbohydrate and low protein sources may be used to supply needed calories and to fulfill essential fatty acid requirements.
Methionaid intake will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development.
Methionaid is best served as a chilled drink with meals. Make a paste of the prescribed amount of powder with a small volume of water. For accuracy, Methionaid should be weighed on a gram scale. Gradually add sufficient water to yield the prescribed volume. It is recommended that Methionaid initially be reconstituted at a 1 to 7 dilution (e.g. 100 g of Methionaid and 700 mL of water). It can however be given in a more concentrated form (e.g. at a 1 to 5 dilution or in paste form), according to taste preferences. Additional fluids should then be offered at the same time.
Reconstituted formula should be stored in the refrigerator and used within 24 hours.
Maxamaid
Range (Flavored & Unflavored)
Measure
Weight
1
Cup
145
g
1/2
Cup
70
g
1/4
Cup
35
g
1
Tbsp
9
g
Precaution:
The recommended dosage of Methionaid is dependent on the age, bodyweight and medical condition of the patient.
Methionaid is best served as a chilled drink with meals. When reconstituting, it is best to make a paste using the prescribed amount of powder and minimal water. Once a paste is made, water should be added gradually to yield the prescribed volume (initially 1 to 7 dilution, i.e. 50g powder plus 350ml of water, building up to a 1 to 5 dilution i.e. 50g powder plus 250ml of water). Mix with blender or beater until thoroughly dissolved. Or, if preferred, may be combined with low protein beverages such as tomato, orange or pineapple juices. Serve as directed by physician. Prepared product not used immediately should be covered, stored in refrigerator and used within 24 hours. Shake well before use.
Storage:
Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.