A methionine-free powdered medical food for the dietary management of vitamin B6 non-responsive homocystinuria or hypermethioninemia in older children and adults, including pregnant women and women of child-bearing age.
This formulation is available in the US and Canada.
Main Features:
Lysine-
and tryptophan-free
Contains
a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, vitamins, minerals and trace elements
XLys,
XTrp Maxamum provides 40 g of protein equivalent per 100
g of powder
Age-appropriate DRI formulation
Pleasant
orange flavored powder
Does
not contain fat thereby allowing greater flexibility in modifying
energy intake
Indications:
Glutaric
acidemia type I
Directions for Preparation and Use:
Maxamum must be consumed in conjunction with natural protein, fluid and
other nutrients in quantities prescribed by a physician or dietitian
to meet protein and general nutrient requirements.
The
recommended intake of Maxamum will vary depending
on the age, bodyweight and medical condition of the individual.
Intake should be adjusted to maintain normal growth and development.
For accuracy, Maxamum should be weighed on a
gram scale. The daily intake of Maxamum should
be divided into equal portions and distributed throughout the
day.
Maxamum is best served with meals. Make a paste of the prescribed
amount of powder with a small volume of chilled water.
Gradually add sufficient water to make the desired volume.
It is recommended that Maxamum be prepared
at a 1 to 7 dilution (e.g. 35 g (approx ¼ cup)
of powder plus 245 mL (approx. 8 fl oz) of water) and
advanced to a 1 to 5 dilution (e.g. 35 g (approx ¼
cup) of powder plus 175 mL (approx. 6 fl oz) of water).
These dilutions are guidelines only. Maxamum may be given in a more concentrated form (e.g. drink or
paste). If so, water or diluted drinks should be offered
at the same time. For best taste, consume immediately.
Larger volumes of prepared drink mix should be refrigerated
and used within 24 hours or preparation.
Maxamum
Range (Flavored & Unflavored)
Measure
Weight
1
Cup
145
g
1/2
Cup
70
g
1/4
Cup
35
g
1
Tbsp
9
g
Precaution:
Must only be consumed
by individuals with proven glutaric acidemia type 1 while
under strict medical supervision. Not intended for children
under nine years of age. Not suitable as a sole source
of nutrition. Not for parenteral use.
Storage:
Store
unopened can at room temperature. Do not store at extreme
temperatures. Once opened, reseal can and store in a cool,
dry place (not in refrigerator) and use within one month.
Metabolics
