A methionine- and cysteine-free powedered infant formula for the dietary management of conditions requiring restriction of methionine and cystine (e.g. sulphite oxidase deficiency).
This formulation is available in the US and Canada.
Main Features:
Methionine- and cystine free unflavored powder
Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements (including iron, selenium and chromium)
XMet XCys Analog provides 13 g of protein equivalent per 100 g of powder
Osmolality (at 15% w/v) = 353 mOsm/kg
Indications:
Sulphite oxidase deficiency
Other conditions requiring restriction of methionine and cystine
Directions for Preparation and Use:
Analog metabolic infant formulas must be consumed in conjunction with a whole protein source (e.g. breast milk or standard infant formula) in quantities prescribed by a dietitian or physician to meet complete protein requirements and ensure normal growth.
Formula dosage will vary depending on the age, body weight, medical condition and protein tolerance of the infant.
Boil water for 5 minutes and allow to cool for at least 30 minutes so that it feels warm to the wrist.
Add the prescribed amount of Analog powder and a protein source to the sterilized feeding bottle. For accuracy, Analog should be weighed on a gram scale. If using the provided scoop, fill it and level off with a clean, dry knife. Do not press the powder into the scoop.
Pour the required amount of cooled, boiled water into feeding bottle. To make the recommended dilution (21 kcal/oz), Analog requires 1 fl oz (30 mL) of water for every 5 g (1 unpacked, level scoop) of powder. Place cap on bottle and shake until powder has dissolved.
Make sure the formula is lukewarm by placing a few drops on your wrist.
Formula prepared in advance must be cooled rapidly, stored in the refrigerator (35°F to 40°F) and used within 24 hours of preparation. Shake immediately before use. Formula remaining in the bottle after one hour of feeding should be discarded. Tube feeding "hang time" should not exceed 4 hours.
Analog
Range
Measure
Weight
1 Scoop
5 g
1
Cup
115
g
1/2
Cup
55
g
1/4
Cup
30
g
1
Tbsp
8
g
Precaution:
Must only be used under strict medical supervision. Not intended as the sole source of nutrition. Not for parenteral use. XMet XCys Analog should not be used as the sole source of protein but must be given in conjunction with a protein source e.g. breast milk or proprietary infant formula to supply the methionine, cystine and general nutritional requirements of the patient.
Storage:
Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.
Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation. Stir or shake immediately before use.