An unflavored phenylalanine- and tyrosine-free
powdered product for the dietary management of tyrosinemia type
2 in children 8 years and older and adults, including pregnant
women and women of child-bearing age.
This formulation is only available in Canada.
Main Features:
Phenylalanine- and tyrosine-free
Contains a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, vitamins, minerals and trace elements
XPhen, Tyr Maxamum provides 39 g of protein equivalent per
100 g of powder
Does not contain fat thereby allowing greater flexibility
in modifying energy intake
Osmolality:
Dilution
1 to 7
690 mOsm/kg
1 to 5
1000 mOsm/kg
Indications:
Tyrosinemia type 2
Directions for Preparation and Use:
Maxamum must be consumed in conjunction
with natural protein, fluid and other nutrients in quantities
prescribed by a dietitian or physician to meet protein and
general nutrition requirements. Fat, carbohydrate and low protein
sources may be used to supply needed calories and to fulfill
essential fatty acid requirements.
Maxamum intake will vary depending on the age, body weight
and medical condition of the individual. Intake is adjusted
to maintain normal growth and development.
Maxamum is best served as a chilled drink with meals. Make
a paste of the prescribed amount of powder with a small volume
of water. For accuracy, Maxamum should be weighed on a gram scale.
Gradually add sufficient water to yield the prescribed volume.
It is recommended that Maxamum initially be reconstituted at
a 1 to 7 dilution (e.g. 100 g of Maxamum and 700 mL of water).
It can however be given in a more concentrated form (e.g. at
a 1 to 5 dilution or in paste form), according to taste preferences.
Additional fluids should then be offered at the same time.
Reconstituted formula should be stored in the refrigerator
and used within 24 hours.
Measure
Weight
1
Cup
145
g
1/2
Cup
70
g
1/4
Cup
35
g
1
Tbsp
9
g
Precaution:
Must only be consumed by children
with proven tyrosinemia while under strict medical supervision.
Not intended for children under one year of age. Not
suitable as a sole source of nutrition. Not for parenteral
use.
Storage:
Store unopened can at room temperature.
Do not store at extreme temperatures. Once opened, reseal
can and store in a cool, dry place (not in refrigerator)
and use within one month.
Ordering Information:
Product
Code
Packaging
11203
3 x 500 g (17.6 oz)
For product information or to place an
order please call 1-877-636-2283 or fax 514-745-6625 Monday
to Friday, 8:30 to 5:00 EST.
Metabolics
